BBOX1

Gene Symbol BBOX1
Entrez Gene 8424
Alt Symbol BBH, BBOX, G-BBH, gamma-BBH
Species Human
Gene Type protein-coding
Description butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
Other Description gamma-butyrobetaine dioxygenase|gamma-butyrobetaine hydroxylase|gamma-butyrobetaine,2-oxoglutarate dioxygenase 1
Swissprots O75936 Q6IBJ2 B2R8L7 D3DQZ1
Accessions EAW68290 EAW68291 O75936 AF082868 AAC64066 AK290108 BAF82797 AK313422 BAG36214 BC011034 AAH11034 CR456812 CAG33093 DA268467 DQ471856 ABF17859 DQ471857 ABF17860 DQ471858 ABF17861 DQ471859 ABF17862 DQ471860 ABF17863 DQ471861 ABF17864 DQ471862 ABF17865 DQ471863 ABF17866 DQ471864 ABF17867 DQ471865 ABF17868 DQ471866 ABF17869 DQ471867 ABF17870 DQ471868 ABF17871 DQ471869 DQ471870 DQ892777 ABM83703 DQ896024 ABM87023 EU831621 ACE87221 XM_005253159 XP_005253216 XM_005253160 XP_005253217 XM_005253161 XP_005253218 XM_011520402 XP_011518704 XM_011520403 XP_011518705 NM_003986 NP_003977
Function Catalyzes the formation of L-carnitine from gamma- butyrobetaine.
Subcellular Location Cytoplasm.
Tissue Specificity Highly expressed in kidney; moderately expressed in liver; very low expression in brain.
Top Pathways Lysine degradation

BBOX1 CRISPR/Cas9 KO Plasmid (h) - sc-411174 from Santa Cruz Biotechnology

Category CRISPR
Prices $345.00
Sizes 20 µg
Species Reactivities Human

BBOX1 HDR Plasmid (h) - sc-411174-HDR from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

BBOX1 Double Nickase Plasmid (h) - sc-411174-NIC from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

BBOX1 Double Nickase Plasmid (h2) - sc-411174-NIC-2 from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

BBOX1 CRISPR Activation Plasmid (h) - sc-411174-ACT from Santa Cruz Biotechnology

Category CRISPR
Prices $345.00
Sizes 20 µg
Species Reactivities Human

BBOX1 CRISPR Activation Plasmid (h2) - sc-411174-ACT-2 from Santa Cruz Biotechnology

Category CRISPR
Prices $345.00
Sizes 20 µg
Species Reactivities Human

BBOX1 Lentiviral Activation Particles (h) - sc-411174-LAC from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

BBOX1 Lentiviral Activation Particles (h2) - sc-411174-LAC-2 from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

BBOX1 siRNA (h) - sc-96811 from Santa Cruz Biotechnology

Category siRNA
Prices $258.00
Sizes 10 µm
Species Reactivities Human

BBOX1 shRNA Plasmid (h) - sc-96811-SH from Santa Cruz Biotechnology

Category siRNA
Prices $258.00
Sizes 10 µm
Species Reactivities Human

BBOX1 shRNA (h) Lentiviral Particles - sc-96811-V from Santa Cruz Biotechnology

Category siRNA
Prices $258.00
Sizes 10 µm
Species Reactivities Human

BBOX1 RNAi - H00008424-R01 from Novus Biologicals

Category siRNA
Prices $399.00
Sizes 20 nmol
Species Reactivities Human

MISSION® esiRNA - EHU136061 from Sigma-Aldrich

Category siRNA
Prices $140.00, $250.00
Sizes 20 µg, 50 µg

CompoZr® Knockout ZFN Kit - CKOZFN3876 from Sigma-Aldrich

Category ZFN Kit
Prices $4,999.00
Sizes 1 kt

CompoZr® Knockout ZFN Kit, ZFN plasmid only - CKOZFND3876 from Sigma-Aldrich

Category ZFN Kit
Prices $3,999.00
Sizes 1 kt

MISSION® 3′UTR Lenti GoClone™ - HUTR02724 from Sigma-Aldrich

Category miRNA
Prices $350.00
Sizes hutr02724

BBOX1 siRNA (Human) - CRH5518 from Cohesion Biosciences

Category siRNA
Prices $340.00, $510.00
Sizes 15 nmol, 30 nmol
Species Reactivities Human

BBOX1 - MBS829922 from MyBioSource

Prices $365.00, $515.00
Sizes 15 nmol, 30 nmol
Species Reactivities Human

shRNA set against Human BBOX1 (NM_003986.2) - SHH245094 from Creative biogene

Category siRNA
Species Reactivities Human

shRNA set against Human BBOX1(NM_003986.2) - SHG092267 from Creative biogene

Category siRNA
Species Reactivities Human

Human BBOX1 siRNA - orb266020 from Biorbyt

Category siRNA
Prices $485.00, $629.00
Sizes 15 nmol, 30 nmol
Species Reactivities Human

BBOX1 shRNA Plasmid (Human) - CHH5518 from Cohesion Biosciences

Category siRNA
Prices $500.00, $750.00
Sizes 150 µg, 300 µg
Species Reactivities Human

BBOX1 miRNA 3'UTR clone - MiUTR1H-00821 from Creative biogene

Species Reactivities Human
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